Feature |
CPS-l |
CPS-ll |
Full Name |
Carbamoyl Phosphate |
Carbamoyl Phosphate |
Location |
Mitochondria |
Cytosol |
Pathway |
Urea Cycle |
Pyrimidine Synthesis |
Substrate |
Ammonia (NH3) |
Glutamine (Gln) |
Activator |
N-Acetylglutamate (NAG) |
PRPP (Phosphoribosyl |
Function |
Converts ammonia and bicarbonate |
Converts glutamine and bicarbonate |
Expression |
Primarily in liver |
Found in many tissues |
Clinical |
Deficiency can lead to |
Important for DNA and |